Cystic fibrosis drugs rejected for use in Scotland

The SMC said it heard “strong evidence” from patient groups and recognised that the decision would be “disappointing”. ‘Deadlock must end’ over cystic fibrosis drug Orkambi Cystic fibrosis drug campaign makes no progress in year But chairman Dr Alan MacDonald said: “There remained significant uncertainty around their overall health benefits in the long-term, in relation to their costs. “In order to be able to accept these medicines the committee will need to be satisfied of their cost-effectiveness and we continue to work with the company to achieve that.” ‘It’s not a pretty thing to watch’ Image copyright SPL Manufacturer Vertex said it hoped to find a solution which would allow broad access to the drugs in the coming weeks. In …

Government launches investigation into power cut

The Energy Emergencies Executive Committee, carrying out the inquiry, will also explore whether there were any technical problems, plus how well National Grid communicated about the incident and restored the problem. National Grid’s director of operations Duncan Burt said he did not believe that a cyber-attack or unpredictable wind power generation was to blame. Speaking on BBC Radio 4’s Today programme on Saturday, Mr Burt acknowledged the “immense disruption” the blackout had caused. He said the near-simultaneous loss of two generators was more than the grid was routinely prepared for, prompting automatic safety systems to shut off power to some places. “We think that worked well; we think the safety protection systems across the industry, on generators and on the …

Gangs moving away from cities, police data shows

But just 20 miles away in Westminster, central London, drug crime more than halved over the same period, from 4,041 to 1,832. The pattern is repeated in many other areas around the capital, a BBC analysis of police-recorded crime showed. Sorry, your browser cannot display this map The map above used a statistical model to classify areas that have experienced a significant change in drug crime. Weight is given to areas with a strong overall trend of increasing or decreasing crime across several years. Where there is no strong overall pattern in a particular location, those areas have been labelled as having “no change”. Tap here if you can’t see the interactive map above In Liverpool drug crime has fallen …

Gambling companies see huge rise in complaints

Media playback is unsupported on your device Media caption“If I hadn’t gone online for a day, they were quickly on the phone or sending me an email” The number of gamblers complaining about British betting firms has risen almost 5,000% in the past five years. There were a record 8,266 complaints last year, according to Gambling Commission figures obtained by BBC Panorama. That compares to just 169 in 2013. Most of them were about firms refusing to pay out on winning bets or failing to operate in a socially responsible way. The rise follows a sharp increase in UK gambling over the past decade. Image caption Neil McArthur says the industry must know its customers “We are pushing the industry …

Ambulance crew shortage expected for third night

The service had appealed for staff to come to work at the weekend because of difficulties filling rotas. “We are doing everything we can to provide as high a level of cover as we can,” said Dr Ruddell. “We are going to prioritise those calls which have the most critical need. “Unfortunately, those people who have a less critical need are the ones who wait longer, and we apologise for that.” Related Topics NI Health UK ambulance services Northern Ireland Ambulance Service Original Article : HERE ;

UK house prices and sales ‘losing momentum’

Britain’s fastest moving property market revealed Letting fees ban: Renters confused after change in law Rics said 69% of property professionals said sale prices were lower than asking prices for homes marketed at more than £1m, although asking prices for homes priced at £500,000 or less appeared to be holding up more firmly. House prices continued to fall in London – where a higher proportion of £1m homes are sold, the South East of England, and East Anglia. Overall across the survey, a net balance of 9% of surveyors reported house prices falling rather than increasing. Surveyors’ expectations for house sales in the next few months were flat, with an increasing proportion expecting prices to fall, the survey showed. Simon …

‘I was denied screening because of my disability’

When Kerry Thompson, 40, from Milton Keynes, who has muscular dystrophy, was told she could no longer have cancer screening at home when she moved house. This was despite the test showing up abnormalities that needed regular appointments. Gay women ‘at risk of cervical cancer too’ What happens during a smear test ‘This is for anyone with a vagina’ ‘Nothing they could do’ “I had a new GP and I explained the situation – that the rooms were too small for my wheelchair to fit in and there was no hoist or wide bed for me to use,” she said. “I also would need two nurses to help hold my legs, which can flop over. “I can’t be the only …

Thousands of fans rock out at Bloodstock 2019

Image copyright Katja Ogrin Image caption The crowds rocked to the ear-shattering line-up Image copyright Down The Barrel Photography Image caption Campers enjoyed the dry weather before heavy downpours began on Friday Image copyright Katja Ogrin Image caption Diehard metal fans were head-banging to the likes of Sabaton, Powerwolf, and Metal Church Image copyright Katja Ogrin Image caption Revellers planned for a wild knight Image copyright Tim Finch Image caption Fans were happy to battle the wind and rain to see some of their favourite metal bands Related Topics Swadlincote Original Article : HERE ;

Why do Welsh place names appear around the world?

Image caption This map shows just a few of the Welsh place names around the world The story involves a Welshman who played a major role in extending the American Civil War and a Swansea businessman who built a copper smelting plant in the Arizonan desert. Dr Matthews said the biggest wave of Welsh emigration came in the late 19th Century. Image copyright Gethin Matthews Image caption Swansea appears across the USA and Australia, including here in Tasmania Many of these places were likely given their names during the first wave of religious migrants between 1682 and 1700. But the figures are sketchy. For example, estimates of the number of Welsh people who emigrated to the United States between 1820 …

Flooding causes major disruption across North

Motorists were urged to drive only if “absolutely necessary”, and Poynton’s town clerk said people affected by the flooding were welcome at the town’s civic hall. Neil Griffiths, from Cheshire Fire and Rescue Service, said flood waters were beginning to recede on Thursday night. At the scene Richard Stead, BBC Manchester, in Bramhall, Stockport The weather has been horrendous here; we have had torrential rain all day. At the main Bramhall roundabout, where three roads meet, there is currently a lake about two feet deep. Two men were paddling around in a canoe and were told to get out of the water by angry firefighters. If they fell in, the firefighters would have had to rescue them. Derbyshire Police said …

Woman told to reveal source of ‘unexplained’ 3.2m

She was served with the unexplained wealth order (UWO) by the NCA on Tuesday. Andy Lewis, Head of Asset Denial at the NCA, said it is only the fourth case of a UWO in the UK. “Our investigations are complex and involve careful consideration before we make an application before the court,” Mr Lewis said. “We do not investigate illicit finance based on monetary value alone. This latest order shows that we will act against those who we believe are causing the most harm to our communities.” The NCA said no further details can be released which may lead to the identification of the properties or the people who own them.

Corbyn demands fracking ban at protest

He said Labour would ban fracking and instead focus on creating a “green industrial revolution”, which would include investment in tidal power. “We need urgent action to tackle the climate emergency, and that means the Prime Minister immediately banning fracking once and for all,” he said. Image copyright PA Media Image caption Fracking at the Preston New Road site is expected to resume next month The Preston New Road site began fracking in October but operations were halted on a number of occasions due to underground tremors. Cuadrilla said it expects to resume fracking by the end of August. Hydraulic fracturing, or fracking, is a technique to extract gas and oil from the earth Liquid is pumped underground at high …

Ministers reject troubled shipyard offer

It also presented legal advice, commissioned by Clyde Blowers Capital, that the proposed deal would be within European rules on procurement and state aid – the extent to which governments are allowed to intervene in support of businesses. That advice has been flatly rejected by the Scottish government, saying it is obliged to seek the lowest cost option. The dispute could lead to it using a clause in the £45m of loan agreements between the Scottish government and Ferguson Marine Engineering Limited (FMEL), through which it could take over the yard for only £1. It is understood that a separate private lender debt, providing a £25m bond required of FMEL to ensure delivery of the ferries, is secured against ownership …

Man freed from rocks ‘nearly a different story’

“The tide subsided enough that we managed to release his leg from his cast through brute force but if there was half-an-hour difference in timing, it could have been a very different story. “He was stuck for three hours or more but stayed so positive throughout and really helped us through the incident.” The man had been leaving the beach with his family when one of his two children slipped on rocks near the town’s East Promenade. Then, as he stepped over to grab the toddler, the man fell and became stuck. HM Coastguard and Sheringham RNLI co-ordinated the rescue effort after the alarm was raised at 17:30 BST. The coastguard originally reported the man was in his 20s. The …

Woman ‘may have been killed with lava lamp cable’

On the day she died, Mr Andrews made a 999 call and said: “My partner’s dead, I strangled her.” He also sent a Facebook message to her new boyfriend Robert Morris saying: “You won’t see Lana again she’s dead”, and confessed the crime to police “without any emotion whatsoever”. Mr Morris said he tried to persuade Ms Owen not to go and talk to Mr Andrews on the day she died, but she “didn’t want to be horrible to him” and so he took her home that morning. Ms Owen’s son Corey Hill told the inquest he had never been aware of any violence before his mother died. Related Topics Tonypandy Pontypridd Original Article : HERE ;